Vol.98No.9contentsPRACTICA OTO-RHINO-LARYNGOLOGICA
Vol. 98 No. 9 September 2005
Two Cases Report of Arnold-Chiari Malformation
with Neuro-Otological Examination
Yoshiya Ishida and Hiroshi Shigyo
(Hokkaido Social Insurance Hospital, Asahikawa Medical College)
Takeshi Kanaya
(Hokkaido Social Insurance Hospital)
Yasuaki Harabuchi
(Asahikawa Medical College)
Arnold-Chiari malformation is a rare congenital condition characterized by varying degrees of downward displacement of the cerebellar tonsils, inferior cerebellum or medulla through the foramen magnum. Diagnosis of Arnold-Chiari malformation is not difficult due to the characteristic primary position downbeat nystagmus and a variety of cerebellar signs. Recently using magnetic resonance imaging (MRI), diagnosis of Arnold-Chiari malformation is more easy, but the degree of neurological disorder in the cerebellum and brainstem are not clarified without neuro-otological examination. We analyzed the eye movement using electro-nystagmograph in two cases of Arnold-Chiari malformation (one case is 14 old female and the other case is 54 old female) and discussed the differences of neuro-functional disorder between two cases that can not be discriminated by MRI techniques only.
Key words : Arnold-Chiari malformation, downbeat nystagmus, postcaloric secondary phase nystagmus,
neuro-otological
examination